Topic: Congenital Hepatic Fibrosis and Autosomal Recessive Polycystic Kidney

Congenital Hepatic Fibrosis and Autosomal Recessive Polycystic Kidney Disease: An Analytic Review of the Literature.

"Cholangiocarcinoma (CCA) was predominant in individuals over the age of 40 with either Caroli's syndrome or isolated CHF, not ARPKD (median and mean age at CCA diagnosis were 70.3 and 60.1 years; respectively, range 33 - 75 years)."

http://www.ncbi.nlm.nih.gov/pubmed/2219 … t=Abstract